A child with cPAN as only manifestation of FMF

Introduction Cutaneous Polyarteritis Nodosa (cPAN) is a rare type of vasculitis affecting small-to-medium-size arteries. It is distinct from systemic PAN in that it lacks significant internal organ involvement. Familial Mediterranean Fever (FMF) is the most common inherited autoinflammatory disease, characterized by recurrent, self–limited attacks of fever and aseptic polyserositis. PAN is considered one of the four types of vasculitis associated with FMF. FMF is widespread in Armenia and there is a higher than expected frequency of FMF-associated vasculitis which may in some cases be the first indication for MEFV mutation analysis.